Arrhythmogenic Right Ventricular Hypertrophy

This is an autosomal dominant disease with variable penetration that is second only to HCM in causing sudden cardiac death in otherwise healthy young people.  Dr. Burns presents basic ECG findings of ARVH as well as discussing other diagnostic studies and treatment.  Highlights below.

• Epsilon wave: positive deflection buried in end of QRS complex, occasionally resembling greek letter epsilon on its side.
• T wave inversions in V1-3
• Prolonged S wave upstroke of 55ms in V1-3
• Wide QRS in V 1-3
• Paroxysmal VTach with LBBB morphology

Copa Cardiogram #79